Diagnostic criteria for idiopathic pulmonary fibrosis: a Fleischner Society White Paper.

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Title: Diagnostic criteria for idiopathic pulmonary fibrosis: a Fleischner Society White Paper.
Author(s): Lynch, DA
Sverzellati, N
Travis, WD
Brown, KK
Colby, TV
Galvin, JR
Goldin, JG
Hansell, DM
Inoue, Y
Johkoh, T
Nicholson, AG
Knight, SL
Raoof, S
Richeldi, L
Ryerson, CJ
Ryu, JH
Wells, AU
Item Type: Journal Article
Abstract: This Review provides an updated approach to the diagnosis of idiopathic pulmonary fibrosis (IPF), based on a systematic search of the medical literature and the expert opinion of members of the Fleischner Society. A checklist is provided for the clinical evaluation of patients with suspected usual interstitial pneumonia (UIP). The role of CT is expanded to permit diagnosis of IPF without surgical lung biopsy in select cases when CT shows a probable UIP pattern. Additional investigations, including surgical lung biopsy, should be considered in patients with either clinical or CT findings that are indeterminate for IPF. A multidisciplinary approach is particularly important when deciding to perform additional diagnostic assessments, integrating biopsy results with clinical and CT features, and establishing a working diagnosis of IPF if lung tissue is not available. A working diagnosis of IPF should be reviewed at regular intervals since the diagnosis might change. Criteria are presented to establish confident and working diagnoses of IPF.
Publication Date: 15-Nov-2017
Date of Acceptance: 6-Oct-2017
URI: http://hdl.handle.net/10044/1/56696
DOI: https://dx.doi.org/10.1016/S2213-2600(17)30433-2
ISSN: 2213-2600
Publisher: Elsevier
Start Page: 138
End Page: 153
Journal / Book Title: Lancet Respiratory Medicine
Volume: 6
Issue: 2
Copyright Statement: © 2017, Elsevier. Licensed under the Creative Commons Attribution-NonCommercial-NoDerivatives 4.0 International http://creativecommons.org/licenses/by-nc-nd/4.0/
Publication Status: Published online
Appears in Collections:National Heart and Lung Institute
Airway Disease
Faculty of Medicine



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