Dieulafoy's disease (DD) is characterized by the presence of an anomalous blood vessel within the submucosa, sometimes presenting with life-threatening haemorrhages. Firstly described in the stomach in 1898, this condition has been occasionally reported in the respiratory system [1] and,following a recent case in our institution, we performed a systematic analysis of the literature from 1995 to 2015 on articles describing cases involving the bronchial tree to look at criteria for diagnosis and management. This article is protected by copyright. All rights reserved.